3-Hydroxyisovalerylcarnitine
Catalog No.
BA7605
3-Hydroxyisovalerylcarnitine is a carnitine derivative.
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3-Hydroxyisovalerylcarnitine is a carnitine derivative. Plasma 3-Hydroxyisovalerylcarnitine serves as a novel biomarker of biotin deficiency in humans, and its concentration increases with biotin deficiency. Biotin deficiency decreases the activity of biotin-dependent 3-methylcrotonyl-CoA carboxylase, impairs the conversion of 3-methylcrotonyl-CoA to 3-methylglutaconyl-CoA, and impairs the leucine catabolic pathway; resulting in a decrease in plasma 3- Hydroxyisovalerylcarnitine concentration is elevated.
| Physical Appearance | A solid |
| Storage | -20°C, protect from light |
| M.Wt | 261.31 |
| Cas No. | 99159-87-2 |
| Formula | C12H23NO5 |
| Shipping Condition | Small Molecules with Blue Ice, Modified Nucleotides with Dry Ice. |
| General tips | We do not recommend long-term storage for the solution, please use it up soon. |